Congenital heart disease

Perfusfind S.L.

Eisenmenger syndrome is the most severe form of pulmonary arterial hypertension and arises on the basis of congenital heart disease with a systemic-to-pulmonary shunt. Due to the chronic slow progressive hypoxemia with central cyanosis, adult patients with the Eisenmenger syndrome suffer from a complex and multisystemic disorder including coagulation disorders..

Perfusfind S.L.

Development of Eisenmenger syndrome in a known patient of patent ductus arteriosus (PDA) is easy by carefully looking for differential cyanosis and clubbing in upper and lower limbs. It is quite uncommon for a patient of PDA to present primarily after development of Eisenmenger syndrome. We report a 35-year-old male..

Perfusfind S.L.

Eisenmenger syndrome (ES) is a constellation of symptoms that arise from a congenital heart defect and result in large anatomic shunts. Due to anatomic variations present at birth, hemodynamic forces initially result in a left-right shunt, which develops into severe pulmonary arterial hypertension (PAH) and elevated vascular resistance. Ultimately, due..

Perfusfind S.L.

Atrial septal defect (ASD) may be rarely associated with Eisenmenger syndrome (ES), the most advanced form of pulmonary vascular disease to complicate a congenital heart disease. In spite of availability of pediatric cardiologists and two-dimensional-echochardiography in many tertiary health care centers in Nigeria, late referral and late diagnosis of ASD..

Perfusfind S.L.

An aortopulmonary (AP) window is a rare cause of Eisenmenger syndrome and results from an abnormal septation of the truncus arteriosus [1]. Most such defects present with early onset congestive heart failure during infancy and adult survival in surgically uncorrected patients is rare 2, 3. An aortopulmonary window (APW) is a rare congenital heart defect involving..

Perfusfind S.L.

The Ebstein's anomaly is a malformation of the tricuspid valve, in which the septal and posterior leaflets are attached to the wall of the right ventricle. The usual association is with an atrial septal defect, followed by pulmonary stenosis and pulmonary atresia; the ventricular septal defect is unusual.

Perfusfind S.L.

A malformed heart valve that does not properly close to keep the blood flow moving in the right direction. Blood may leak back from the lower to upper chambers on the right side of the heart. This syndrome also is commonly seen with an , or ASD (or a hole in the..

Perfusfind S.L.

Ebstein’s anomaly is a rare congenital heart disorder occurring in ≈1 per 200 000 live births and accounting for <1% of all cases of congenital heart disease. This anomaly was described by Wilhelm Ebstein in 1866 in a report titled, “Concerning a very rare case of insufficiency of the tricuspid valve..

Perfusfind S.L.

Mitral valve dysplasia syndrome is a unique form of congenital heart disease with severe aortic stenosis but normal or enlarged left ventricle secondary to primary mitral valve disease. Increased left heart size and pulmonary vein Doppler patterns are predictive of postnatal outcome. Despite the presence of a dilated left ventricle,..

Perfusfind S.L.

Transposition of the great arteries (TGA) is a pediatric cardiac congenital defect arising from an embryological discordance between the aorta and pulmonary trunk. During cardiac development, the conotruncal septum spirals toward the aortic sac thus dividing the truncus arteriosus into the pulmonary and aortic channels. These channels then become the..