Eisenmenger syndrome with atrioventricular septal defect (AVSD)

Eisenmenger syndrome (ES) is a constellation of symptoms that arise from a congenital heart defect and result in large anatomic shunts. Due to anatomic variations present at birth, hemodynamic forces initially result in a left-right shunt, which develops into severe pulmonary arterial hypertension (PAH) and elevated vascular resistance. Ultimately, due to increased pulmonary vascular resistance, the left-to-right shunt will become a right-to-left shunt, resulting in significant hypoxemia and cyanosis. This activity a discussion of the evaluation and treatment of Eisenmenger syndrome and further defines the role of the interprofessional team in managing patients with this condition.

Objectives:

• Review the pathophysiology of Eisenmenger Syndrome.
• Identify patients considered high risk for Eisenmenger Syndrome
• Describe the physical exam findings associated with Eisenmenger Syndrome.
• Summarize the importance of improving care coordination amongst the interprofessional team to enhance delivery of care for patients affected with Eisenmenger Syndrome.