Tags Archives: congenital cardiopathies

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Supravalvular mitral ring with mitral stenosis

Supravalvar mitral ring is a circumferential ridge or membrane arising from the left atrial wall overlying the mitral valve and frequently attached to the mitral valve. Variable in thickness and extent,..

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Inferior sinus venosus defect (SVD) with partial anomalous pulmonary venous connection (PAPVC)

Background Sinus venosus defect (SVD) is an unusual type of interatrial communication (IAC) and is virtually always associated with partial anomalous pulmonary venous drainage (PAPVD) of the right pulmonary veins..

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Muscular ventricular septal defect (VSD)

A ventricular septal defect (VSD) is a communication between the interventricular chambers. Muscular ventricular septal defects have exclusively muscular borders and are more likely to be multiple. Their location and..

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Muscular ventricular septal defect (VSD) with left ventricular dilatation

A ventricular septal defect (VSD) is an opening in the interventricular septum, causing a shunt between ventricles. Large defects result in a significant left-to-right shunt and cause dyspnea with feeding..

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Perimembranous ventricular septal defect (VSD)

Perimembranous ventricular septal defects (VSDs) are located in the left ventricle outflow tract beneath the aortic valve. They are the most common  subtype in the United States, occurring in 75-80% of..

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Perimembranous ventricular septal defect (VSD) with ventricular dilatation

Perimembranous ventricular septal defects (VSDs) are located in the left ventricle outflow tract beneath the aortic valve. They are the most common VSD subtype in the United States, occurring in 75-80% of cases. Defects may extend into..

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Doubly committed ventricular septal defect (VSD)

Doubly committed subarterial ventricular septal defect (VSD) is a unique type of VSD, located beneath the aortic and pulmonary valves, accounting for about 5–7% of all VSD autopsy findings. It is also called supracristal or infundibular VSD..

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Doubly committed ventricular septal defect (VSD) with ventricular dilatation

Background: The morphology of ventricular septal defects (VSDs) that are doubly committed and juxtaarterial places the patient at risk for aortic valvar prolapse and aortic valvar insufficiency (AI). Surgical repair of..

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Complete atrioventricular septal defect (AVSD)

Atrioventricular septal defects (AVSD) are a relatively common family of congenital heart defects. Also known as atrioventricular canal defects or endocardial cushion defects, they account for about 5 percent of..

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Complete atrioventricular septal defect (AVSD) with tetralogy of Fallot

Female infant; born on term with 2.6 kg, normal delivery. Mother; fourth pregnancy, denied the use of medication during pregnancy. Presented respiratory discomfort at birth, evolving with neonatal infection and..

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Unbalanced complete atrioventricular septal defect (AVSD) with right dominance

Background: Management of right-dominant atrioventricular septal defect (AVSD) remains a challenge given the spectrum of ventricular hypoplasia. The purpose of this study was to assess whether reported echocardiographic indices and additional..

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Unbalanced complete atrioventricular septal defect (AVSD) with right dominance

Unbalance in atrioventricular septal defect can be found in more than one anatomic level and in different degrees at each level. The definition of “unbalance” has historically been focused in..

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Complete atrioventricular septal defect (AVSD) with tetralogy of Fallot and pulmonary stenosis

Repair for tetralogy of Fallot (TOF) with complete atrioventricular septal defect (CAVSD) has been reported with good early and intermediate outcomes. Morbidity, however, remains significantly high. To date, repair of..

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Partial atrioventricular septal defect (ASD Type I, Ostium primum defect)

Atrioventricular (AV) septal defect consists of an ostium primum type atrial septal defect and a common AV valve, with or without an associated inlet (AV septal type) ventricular septal defect..

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Dysplastic mitral valve with mitral stenosis

  syndrome is a unique form of left-sided heart disease characterized by aortic outflow , dilated , dysplastic/incompetent mitral valve, and a restrictive/intact . Patients with this constellation of abnormalities have been managed in..

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Parachute mitral valve with mitral stenosis

Congenital  (MS) results from a variety of anatomic anomalies in the pediatric population, and it is commonly associated with parachute  (PMV),,  an abnormality in which the mitral valve (MV) chordae insert into a..

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Levocardia

In levocardia, the heart is predominantly in the left hemithorax with a leftward apex. In , the heart is predominantly in the right hemithorax. Primary dextrocardia is defined as a condition in..

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Inferior sinus venosus defect (SVD)

Inferior sinus venosus defects (SVDs) are rare imperfections located in the inferior portion of the atrial septum, leading to an overriding inferior vena cava (IVC) and an interatrial connection. These..

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Superior sinus venosus defect (SVD) with partial anomalous pulmonary venous connection (PAPVC)

Partial anomalous venous connection (PAPVC) is a rare congenital heart disease where the blood flow from one or more pulmonary veins (but not all) returns to the right atrium or systemic venous circulation and is..

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Superior sinus venosus defect (SVD)

Surgical repair of sinus venosus defect (SVD) with partial anomalous pulmonary venous connection (PAPVC) to the superior vena cava (SVC) or the right atrium (RA) should avoid long term complications..

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Unroofed coronary sinus

Sinus venosus defects (SVDs), originally described in 1858, represent about 2%–10% of all atrial septal defects. The remainder is composed of ostium secundum (70%), ostium primum (20%) and unroofed coronary sinus (<1%)..

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Unroofed coronary sinus with persistent left superior caval vein

The unroofed coronary sinus is a spectrum of cardiac anomalies in which part or all of the common wall between the coronary sinus and the left atrium is absent. Most..

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Atrial septal defect (ASD) Type II

What is it? A "hole" in the wall that separates the top two chambers of the heart. This defect allows oxygen-rich blood to leak into the oxygen-poor blood chambers in..

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Hypoplastic Left Heart Syndrome: A Worldwide Webinar

Part 1 – Introduction and Morphology Part 2 - Surgical Strategies Part 3 - Can We Improve Outcomes Before Birth? Part 4 - Immediate Care After Birth Part 5 -..

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Situs solitus

Visceroatrial situs refers to the position and configuration of the cardiac atria, the tracheobronchial tree, and the thoracoabdominal viscera. Accurate determination of situs is essential because anomalies of situs are..

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