Unroofed coronary sinus

Unroofed coronary sinus syndrome (URCS) is a rare cardiac anomaly in which a communication occurs between the coronary sinus and the left atrium as a result of the partial or complete absence of the roof of the coronary sinus. This entity is strongly associated with a persistent left superior vena cava (LSVC), with or without a connection between both superior venae cavae.¹ The diagnosis of this lesion is important to the prognosis of the patient because of the consequences of brain abscess or cerebral emboli that may result from a right-to-left shunt. However, the diagnosis is often difficult because of nonspecific clinical features. In this report we present our experience with the diagnosis, classification, and surgical treatment of 11 cases of URCS.