Congenital pulmonary anomalies are rare and can vary in their presentation. Unilateral lung agenesis implies absence of lungs and lung blood vessels, whereas the principal bronchus can be absent or hypoplastic [1]. This malformation can occur isolated or associated with other anomalies. Most commonly, these include the elements of the VACTERL syndrome. VACTERL association is a disorder that affects many body systems. VACTERL stands for vertebral defects, anal atresia, cardiac defects, tracheo-esophageal fistula, renal anomalies, and limb abnormalities. Bilateral pulmonary agenesis is condition incompatible with life [2,3]. In this article I would like to present a case of a newborn with left-sided lung agenesis associated with supracardiac type of total anomalous pulmonary venous connection (TAPVC). About 5 such cases are mentioned in literature, so this case is in some sense unique in its presentation.

Andrei Satsuk: Pediatric and adult diagnostic medical sonographer.