Shone Syndrome

Shone syndrome is a collection of eight left-sided obstructive heart lesions. These affect blood flow to and from the left ventricle, or lower left heart chamber.

Shone syndrome was identified by Dr. John Shone in 1953. He described four lesions. Now, eight lesions are considered part of Shone syndrome. A person must have at least three of these lesions to be diagnosed. Of the eight lesions, supra mitral valve, parachute mitral valve, subaortic stenosis, and coarctation of the aorta were the first four described.

Because so many different defects are involved, individuals present in varying ways, with a wide range of combinations of defects, symptoms, and issues. The number of lesions does not necessarily determine the severity of the disease.