Doubled chambered right ventricle

Double-chambered right ventricle (DCRV) was first described in 1858 by TB Peacock, but it is now understood to be a form of congenital heart disease wherein there is a mid-cavitary obstruction that dived the right ventricle into a high-pressure proximal portion and a low-pressure distal portion.[1] DCRV can classify into two main types based on the tissue responsible for the mid-cavitary obstruction. Patients with type 1 DCRV have an anomalous muscle bundle that crosses the right ventricle while type 2 DCRV has parietal and septal muscle hypertrophy that is responsible for the obstruction, and they often are more likely to present with a ventricular septal defect (VSD).[2] Associated anomalies include VSD (most common and can be seen in up to 90% of DCRV patients), transposition of the great arteries, tetralogy of Fallot, ruptured sinus of Valsalva aneurysm, atrial septal defect, aortic valve regurgitation, persistent left superior vena cava, tricuspid valve regurgitation, Ebstein anomaly, and valvar pulmonary stenosis.