Congenitally corrected transposition of the great arteries (ccTGA) with situs inversus

Congenitally corrected transposition of the great arteries (CCTGA) is a rare congenital heart lesion with varied morphological presentation and can often by asymptomatic. A failing systemic right ventricle (RV) or increasing tricuspid regurgitation are generally indications for surgical intervention. The surgical approach depends upon the age of the patient and morphology of the lesion. Anatomical correction is associated with satisfactory long-term results.

Congenitally corrected transposition of the great arteries (CCTGA) is a rare structural heart disease constituting less than 1% of all congenital heart disease (1). It is a unique congenital heart lesion in the sense that despite anatomical aberrations in the form of atrioventricular and ventriculoarterial discordance, there can be physiologically normal circulation without any mixing or shunting of blood. While the indications and techniques for surgical correction of CCTGA continue to evolve, this review seeks to shed light on the rationale and broad principles of surgical intervention that are in vogue today.